A Case of Hepatosplenic γ/δ T-Cell Lymphoma Debuting With Massive Hemoptysis
نویسندگان
چکیده
Summary Hepatosplenic γ/δ T-cell lymphoma (HSTL) is a very rare, aggressive extranodal affecting mainly young adults. Clinically, presents with symptomatic hepatosplenomegaly and systemic symptoms but without lymphadenopathy. The diagnosis confirmed after careful evaluation of bone marrow liver biopsies or, in some cases, diagnostic splenectomy. Overall, survival short regardless chemotherapy regimens applied, including autologous stem cell transplantation. We present case HSTL massive pulmonary hemoptysis requiring bronchial artery embolization.
منابع مشابه
Hepatosplenic γδ T-cell Lymphoma is a Rare Clinicopathologic Entity with Poor Outcome: Report on a Series of 21 Cases. Short title: HEPATOSPLENIC γδ T-CELL LYMPHOMA
We report on the characteristics of 21 cases of Hepatosplenic γδ T-cell lymphoma (HSγδTCL), an entity recognized since 1994 by the REAL classification. Median age was 34 years. Patients presented with splenomegaly (n=21), hepatomegaly (n=15) and thrombocytopenia (n=20). Histopathologic findings were homogeneous with the presence of medium-sized lymphoma cells within the sinusoids of splenic red...
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ژورنال
عنوان ژورنال: Journal of Biomedical and Clinical Research
سال: 2023
ISSN: ['1313-9053', '1313-6917']
DOI: https://doi.org/10.2478/jbcr-2023-0008